Order Entry
Czech Republic
ContactUsLinkComponent
Human recombinant fumarylacetoacetase (from cells)
Human recombinant fumarylacetoacetase (from cells)
Catalog # PRSI91-668
Supplier:  ProSci Inc.
CAS Number:  
Human recombinant fumarylacetoacetase (from cells)
Catalog # PRSI91-668
Supplier:  ProSci Inc.
CAS Number:  

Specifications

  • Bal.:
    50 µG
  • Typ enzymu:
    Recombinant
  • Zdroj:
    Cells
  • Druhy:
    Human
  • Sekvence značek:
    C-6 His tag
  • Podmínky uskladnění:
    Lyophilized protein should be stored at –20 °C, though stable at room temperature for 3 weeks. Reconstituted protein solution can be stored at 4...7 °C for 2 - 7 days. Aliquots of reconstituted samples are stable at –20 °C for 3 months.
  • Název enzymu:
    Fumarylacetoacetase
  • Čistota:
    >95% as determined by reducing SDS-PAGE
  • Molekulární hmotnost:
    47.4 kD
  • Sekvence:
    Ser2-Ser419
  • Formulace:
    Lyophilized from a 0.2 µm filtered solution of PBS. Always centrifuge tubes before opening. Do not mix by vortex or pipetting. It is not recommended to reconstitute to a concentration less than 100 ug/ml. Dissolve the Lyophilized protein in ddH2O. Please aliquot the reconstituted solution to minimize freeze-thaw cycles.
  • Testované aplikace:
    Bioassay

Specifications

About this item

Fumarylacetoacetase belongs to the FAH family. Fumarylacetoacetase is primary expressed in liver and kidney. It exists as a homodimer and catalyses the hydrolysis of 4-fumarylacetoacetate into fumarate and acetoacetate. Defects in Fumarylacetoacetase cause tyrosinemia type 1, which is congenital metabolism defect characterised by elevated levels of tyrosine in the blood and urine, and hepatorenal manifestations. Typical features include renal tubular injury, self-mutilation, hepatic necrosis, episodic weakness, and seizures.

Fusion-Tag: C-6 His tag

This recombinant protein can be used for biological assays. For research use only.